3.A.28.1.5
AAA-ATPase, Bcs1 or Bcs1L of 419 aas and 2 or 3 TMSs. Bcs1 is a chaperone
necessary for the assembly of mitochondrial respiratory chain complex
III. It plays an important role in the maintenance of mitochondrial tubular
networks, respiratory chain assembly and formation of the LETM1
complex 1 (Tamai et al. 2008).
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| Accession Number: | Q9Y276 |
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| Protein Name: | Mitochondrial chaperone BCS1 |
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| Length: | 419 |
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| Molecular Weight: | 47534.00 |
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| Species: | Homo sapiens (Human) [9606] |
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| Number of TMSs: | 1 |
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| Location1 / Topology2 / Orientation3: |
Mitochondrion inner membrane1 / Single-pass membrane protein2 |
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| Substrate |
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1: MPLSDFILAL KDNPYFGAGF GLVGVGTALA LARKGVQLGL VAFRRHYMIT LEVPARDRSY
61: AWLLSWLTRH STRTQHLSVE TSYLQHESGR ISTKFEFVPS PGNHFIWYRG KWIRVERSRE
121: MQMIDLQTGT PWESVTFTAL GTDRKVFFNI LEEARELALQ QEEGKTVMYT AVGSEWRPFG
181: YPRRRRPLNS VVLQQGLADR IVRDVQEFID NPKWYTDRGI PYRRGYLLYG PPGCGKSSFI
241: TALAGELEHS ICLLSLTDSS LSDDRLNHLL SVAPQQSLVL LEDVDAAFLS RDLAVENPVK
301: YQGLGRLTFS GLLNALDGVA STEARIVFMT TNHVDRLDPA LIRPGRVDLK EYVGYCSHWQ
361: LTQMFQRFYP GQAPSLAENF AEHVLRATNQ ISPAQVQGYF MLYKNDPVGA IHNAESLRR